J项目国家先天性免疫缺陷患者护理数据表（2004-2021）

数据集获取（Figshare）

• 源站标题：Table_1_Care of patients with inborn errors of immunity in thirty J Project countries between 2004 and 2021.docx
• DOI：10.3389/fimmu.2022.1032358.s005
• 发布日期：2022-12-16
• 文件数：1 个
• 文件总体积：22.35 KB
• 源站页面：https://frontiersin.figshare.com/articles/dataset/Table_1_Care_of_patients_with_inborn_errors_of_immunity_in_thirty_J_Project_countries_between_2004_and_2021_docx/21739064

命令行下载

curl -L -o "Table_1_Care of patients with inborn errors of immunity in thirty J Project countries between 2004 and 2021.docx" "https://ndownloader.figshare.com/files/38568803"

文件清单

• Table_1_Care of patients with inborn errors of immunity in thirty J Project countries between 2004 and 2021.docx（22.35 KB）

文件总体积 22.35 KB（源站 API 实测）。

数据加载示例（图像类）

from PIL import Image
import glob, os

files = (glob.glob(os.path.join(path, "**", "*.png"), recursive=True)
       + glob.glob(os.path.join(path, "**", "*.jpg"), recursive=True)
       + glob.glob(os.path.join(path, "**", "*.tif"), recursive=True))
print("图像文件数:", len(files))
img = Image.open(files[0]); print("尺寸/模式:", img.size, img.mode)

# torchvision Dataset 方式:
# from torchvision import datasets
# ds = datasets.ImageFolder(path)  # 要求 子目录=类别

目录组织与标注格式以源站说明和下载后实际文件为准。

数据说明

IntroductionThe J Project (JP) physician education and clinical research collaboration program was started in 2004 and includes by now 32 countries mostly in Eastern and Central Europe (ECE). Until the end of 2021, 344 inborn errors of immunity (IEI)-focused meetings were organized by the JP to raise awareness and facilitate the diagnosis and treatment of patients with IEI.
ResultsIn this study, meeting profiles and major diagnostic and treatment parameters were studied. JP center leaders reported patients’ data from 30 countries representing a total population of 506 567 565. Two countries reported patients from JP centers (Konya, Turkey and Cairo University, Egypt). Diagnostic criteria were based on the 2020 update of classification by the IUIS Expert Committee on IEI. The number of JP meetings increased from 6 per year in 2004 and 2005 to 44 and 63 in 2020 and 2021, respectively. The cumulative number of meetings per country varied from 1 to 59 in various countries reflecting partly but not entirely the population of the respective countries. Altogether, 24,879 patients were reported giving an average prevalence of 4.9. Most of the patients had predominantly antibody deficiency (46,32%) followed by patients with combined immunodeficiencies (14.3%). The percentages of patients with bone marrow failure and phenocopies of IEI were less than 1 each. The number of patients was remarkably higher that those reported to the ESID Registry in 13 countries. Immunoglobulin (IgG) substitution was provided to 7,572 patients (5,693 intravenously) and 1,480 patients received hematopoietic stem cell therapy (HSCT). Searching for basic diagnostic parameters revealed the availability of immunochemistry and flow cytometry in 27 and 28 countries, respectively, and targeted gene sequencing and new generation sequencing was available in 21 and 18 countries. The number of IEI centers and experts in the field were 260 and 690, respectively. We found high correlation between the number of IEI centers and patients treated with intravenous IgG (IVIG) (correlation coefficient, cc, 0,916) and with those who were treated with HSCT (cc, 0,905). Similar correlation was found when the number

许可

CC BY 4.0

引用

学术使用请引用 DOI 10.3389/fimmu.2022.1032358.s005（source: https://frontiersin.figshare.com/articles/dataset/Table_1_Care_of_patients_with_inborn_errors_of_immunity_in_thirty_J_Project_countries_between_2004_and_2021_docx/21739064）。