肾病综合征合并原发性非典型溶血性尿毒症综合征

资源简介

肾病综合征合并原发性非典型溶血性尿毒症综合征

【数据集背景】

本数据集源站标题为《Nephrotic syndrome associated with primary atypical hemolytic uremic syndrome》。配套论文《Nephrotic syndrome associated with primary atypical hemolytic uremic syndrome》发表于 Brazilian Journal of Nephrology（2021），DOI：10.1590/2175-8239-jbn-2020-0050。源站首次发布：2022-05-27。

【数据内容】

源站原始描述：Abstract Primary atypical hemolytic-uremic syndrome is a rare disease characterized by non-immune microangiopathic hemolytic anemia, thrombocytopenia, and renal dysfunction; it is related to alterations in the regulation of the alternative pathway of complement due to genetic mutations. The association with nephrotic syndrome is unusual. We present here a pediatric patient diagnosed with primary atypical hemolytic-uremic syndrome associated with nephrotic syndrome who responded to eculizumab tre…

【数据结构与技术规格】

文件数 12 个，合计 57.34 MB。数据集 DOI：10.6084/m9.figshare.19905463.v1。

【主题与分类】

源站学科分类：Nephrology and Urology。主题标签：Atypical Hemolytic Uremic Syndrome、Nephrotic Syndrome、Acute Renal Injury、Hypertension、Complement System Proteins。

【适用方向】

源站学科分类标注为 Nephrology and Urology。

【获取与许可】

源站页面：https://scielo.figshare.com/articles/dataset/Nephrotic_syndrome_associated_with_primary_atypical_hemolytic_uremic_syndrome/19905463

使用许可：CC BY 4.0（https://creativecommons.org/licenses/by/4.0/）。

规范引用：Bello-Marquez, Diana Carolina; Nieto-Rios, John Fredy; Serna-Higuita, Lina Maria; Gonzalez-Vergara, Alfonso Jose (2021). Nephrotic syndrome associated with primary atypical hemolytic uremic syndrome. SciELO journals. Dataset

【使用注意】

· 源站最后修改于 2023-06-15，引用时请注意版本时效。